Congential Long QT syndrome

IDENTIFICATION : E-HOL-03-0480-013

In the mid eighties, Philippe Coumel initiated the systematic recording of Holter ECGs in patients with a prolonged ventricular repolarization.
This Holter database has been nurtured by Isabelle Denjoy, and after discovery of the underlying genetic basis of the syndrome phenotypic ECG data accumulated over 25 years have been linked with the results of genetic data obtained in LQTS patients (N=480).
This primary care-oriented database contains clinical data (demographics, symptomatic status, and beta-blocker treatment at the time of recording) of genotyped LQTS patients who have had one or repeated Holter ECG recording(s).

The distribution of types of LQTS patients in htis database is as follow:

 

ECG files

Subjects

Jervell and Lange-Nielsen

39

24

LQT1

246

171

LQT2

145

89

LQT3

35

14

Others

15

9

 

Number of Leads: 2 or 3 lead Holter ECGs (in case of 2-lead ECGs, the third lead is zeroed)

->Beware ECG ID 387 have incorrect RR annotation file

Sampling Frequency : 200Hz

Amplitude Resolution: available in the ISHNE files

Total Clinical Information available for the database:

Subject
Filename
Gender
Date Of Recording
Symptoms
Therapy
Gene(s)
Mutation(s)
Age